ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA IN CHILDHOOD: DIAGNOSIS, PROGNOSIS AND TREATMENT

Lj. Šulović ,
Lj. Šulović

Medical faculty Priština , Kosovska Mitrovica , Kosovo*

I. Jovanović ,
I. Jovanović

University Hospital of Chlidren , Belgrade , Serbia

M. Đukić ,
M. Đukić

University Hospital of Chlidren , Belgrade , Serbia

V. Parezanović ,
V. Parezanović

University Hospital of Chlidren , Belgrade , Serbia

G. Vukomanović
G. Vukomanović

University Hospital of Chlidren , Belgrade , Serbia

Published: 01.01.2010.

Volume 38, Issue 1 (2010)

pp. 101-103;

https://doi.org/10.70949/pramed201001335S

Abstract

Arrhythmogenic right ventricular dysplasia (ARVD) is a myocardial disease, often familial, that is characterised pathologically by fibrofatty replacement of the right ventricular myocardium, and clinically by ventricular arrhythmias of right ventricular origin which may lead to sudden death, mostly in young people and athletes. The term "dysplasia" was originally used to describe an entity that was considered to be the result of a developmental defect of the right ventricular myocardium.

Keywords

References

1.
Fontaine G, Fontaliran F, Hacbert JL, Chemla D, Zenati O, Lecarpentier Y, et al. Arrhythmogenic right ventricular dysplasia. Annu Rev Med. 50:17–35.
2.
AS AJ. Arrhythmogenic right ventricular dysplasia (ARVD) in childhood: case report with a review of the literature. Annals of Saudi Medicine. 17(3).
3.
Frank R, Fontaine G, Vedel J, Mialet G, Sol C, Guiraudon G, et al. Electrocardiologie de quatre cas de dysplasia ventriculaire droite arrhythmogenique. Arch Mal Cœur. 71:963–72.
4.
Marcus FI, Fontaine GH, Guiraudon G, Frank R, Laurenceau JL, Malergue S, et al. Right ventricular dysplasia. Circulation. 65:384–98.
5.
Ahmad F. The molecular genetics of arrhythmogenic right ventricular dysplasiacardiomyopathy. Clin Invest Med. 26:167–78.
6.
Kayser HW, Wall EE, Sivananthan MU, Plein S, Bloomer TN, Roos A. Diagnosis of arrhythmogenic right ventricular dysplasia: a review. Radiographics. 22:639–50.
7.
O’Donnell D, Cox D, Bourke J, Mitchell L, Furniss S. Clinical and electrophysiological differences between patients with arrhythmogenic right ventricular dysplasia and right ventricular outflow tract tachycardia. Eur Heart J. 24:801–10.
8.
McKenna WJ, Thiene G, Nava A, Fontaliran F, Blomstrom-Lundqvist C, Fontaine G, et al. Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy. Br Heart J. 71:215–8.
9.
Corrado D, Basso C, Thiene G. Arrhythmogenic right ventricular cardiomyopathy: diagnosis, prognosis, and treatment. Education in Heart.

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