Posterior cortical atrophy (PCA) is a slowly progressive dementia characterized by an early onset of visual agnosia, followed by components of Balint's syndrome, Gerstmann's syndrome, and transcortical sensory aphasia. The most striking neuropsychological feature of the syndrome is the dissociation between prominent visuspatial disfunction and relatively preserved memory, personality and insight. PCA is a rare syndrome. Autopsied brains of PCA patients have shown a neuropathology of Alzheimer's disease (AD). PCA is not just AD with prominent visual deficits but a distinct clinical syndrome. Neuropsychological examination is fundamental for the diagnosis. It is very important to assess visuspatial functions. Here we present a case of slowly progressive dementia with visuspatial disturbances and apraxia but relatively preserved memory functions, personality and insight.